CPAM (Congenital pulmonary adenamatoid malfornation) with bronchopulmonary sequestration...
We already knew about the lung tumor, but we just learned about the bronchopulmonary sequestration. What that means is that there is a blood supply from the thoracic aorta that is feeding the tumor in his lung. This blood supply is going through his stomach and diaphragm and attaches to the tumor. Therefore, that means that all of these organs are connected together (sequestration).
First, in the morning I had an MRI, (which I hear Avery was very uncooperative during, which in turn made me have to stay longer and get additional pictures...sigh) followed by a very in depth ultrasound. We had a lunch break, and then met with a social worker. Immediately following was an echocardiogram. (At 25 weeks he weighed in at 2 lbs 1 oz) Avery's heart is completely normal! That was the first good news of the day. Next, met with a genetic counselor that basically told us this is an isolated case and there was nothing we could do to prevent or contribute to his diagnosis.
It sounds scary, but we finally met with the pediatric surgeon at Cincinnati Children's Fetal Care Center. He said that Avery has an "excellent prognosis" so that immediately put us at ease.
So here's what is going to happen:
-I will have regular, routine OB care (WOOHOO) and won't have to go back to Children's while pregnant.
-I can have a normal labor and delivery.
-I can deliver at Kettering!
-At 45 weeks of age Avery will have a CT Scan to confirm that he still has the disorder.
-At 3 months of age he will have surgery (2-3 day hospital stay) to repair the sequestration and remove the tumor. And the most amazing part is that his lung will regenerate and in about 5 weeks it will be like there was never a tumor or a sequestration. He will have a 100% normal, functioning lung and it will be like none of this ever happened!
So, all around great news and my baby boy will be just fine! Thank you God for answering our prayers.